One of the most famous examples of albinism in fiction is
the great white whale in Herman Melville's Moby Dick,
written in 1851. Further evidence of evil associated with
albinism can be found in the novels Jamaica Inn by Daphne Du
Maurier and Deliverance by James Dick. The condition has
often been used in the cinema to create a sense that
provokes our fears of stalkers, assassins, hideousness and
characters that are relentless and impervious to pain.
The word "albino" is considered derogatory by
victims of albinism. Those who have the condition are so few
that writers, filmmakers and TV producers can use this
unfortunate condition to amuse or frighten without fear of
reprisal. And all this in spite of a disability sensitive
movement started over 25 years ago as well as up to date
thinking and actions regarding humanism and political
correctness.
Some say that albinism predates language and community,
but it is still used to strike at our deepest fears. At this
very moment albinism in Tanzania is considered by certain
tribes as agents of demons. With ignorance and prejudice
they are murdering pale eyed and pale skinned inhabitants by
the thousands. It is reported that such a victim may be
cannibalized by his foes in a ritual that removes their
spirit and soul from ever reappearing again in this life or
the life hereafter. Body parts of albinistic victims are
sold and bartered between tribes and villages. The incidence
of albinism in Tanzania is ten times that of any other
region of the world.
Albinism is a result of a genetic process which does not
permit the production of color in organisms. Examples are:
chlorophyll in plants and melanin in people. Melanin
provides, in people, color to the skin, hair and eyes. It
also provides protection from ultraviolet light rays. There
is a complicated series of DNA and chemical formulae that
explains how recessive genes (1 in 70) carried by both
parents causes albinism. This occurs approximately once in
every 17,000 births. Hair color may be white or very light
with light skin and blue or gray eye color. Albinism is
present in every nation, ethnicity or religion. Most parents
have normal coloring. There is a persistent tale that
albinism causes a "red eye" appearance. Actually
the light irides allow the highly vascular retina and
choroid coloration to be seen through the pupil under
certain conditions of lighting such as experienced with
photography.
Most of those affected by albinism are considered
visually disabled. The condition usually results in legal
blindness with best corrected V.A. below 20/200. Abnormal
neurological patterns are present due to lack of pigment in
the foveal area, preventing normal vision and invariably
causing nystagmus and photophobia. One can readily imagine
the handicaps that would befall an albinistic person in the
areas of education, reading, socialization, sports
participation, mobility and peer acceptance. Help is
sometimes available with new technology and vision aids.
There are some who have been able to obtain a driver's
license with V.A. enhancement equipment.
Cases of animal albinism are well documented. The
"red eye" syndrome is usually more apparent than
in humans since the animal eye is smaller and less pigment
is available for protection. The albinistic person or animal
is as healthy as the rest of their species with normal
growth and development. Albinism, by itself, is not life
threatening. However, many animals with albinism do not
possess their natural protective camouflage in nature and
cannot fend for themselves against their predators. Their
survival rate, in the wild, is generally quite low. Some
animal species are intentionally bred to be albinistic and
used in biomedical experiments. The most common lab
specimens are: mice, rabbits, rats, fish and frogs. There
are many others that are also used for such purposes.
There are two more categories of albinism in humans:
oculocutaneous, wherein pigment is lacking in the eye, skin
and hair. (In non-human bodies the results are seen in the
fur, scales or feathers.) In ocular albinism, only the eyes
lack pigment. Albinism can evidence anywhere from no pigment
at all to almost normal levels. People with ocular albinism
have generally normal skin and hair color and may have a
normal eye color appearance. The skin may possess freckles
or moles. In Africa and New Guinea albinism usually produces
red hair, reddish brown skin and blue or gray eyes. Africans
affected with albinism may have yellow hair, pale skin and
blue or gray eyes.
Ocular albinism type 2 is frequently linked to a form of
color blindness and night blindness. Type 3 albinism seems
to be more common among the Amish than in other populations.
A variety of albinism is also associated with hearing loss.
This has been observed predominantly among the Hopi Native
Americans. A complete list of eye conditions prevalent in
albinism must include: nystagmus, amblyopia, refractive
errors (especially astigmatism), photophobia, foveal
hypoplasia, optic nerve hypoplasia, and abnormal crossing of
optic nerve fibers in the chiasm.
Some vision aids recommended should include: eyeglasses
and subnormal vision aids, large print material, closed
captioning, and angled bright reading lights. Help may also
be obtained through strong reading lenses, hand held
magnifiers and projection screens for close work
magnification. Contact lenses may be colored to block
uncomfortable light from irritating the retina with unwanted
glare. Dark sun wear may help albinistics endure outdoor
activities. A rare form of albinism, in addition to the
expected skin and eye problems, causes a greater tendency
toward bleeding disorders, inflammations of the large bowel,
lung disease and kidney problems. In the U.S.A., albinistic
people are expected to have a normal life span as opposed to
the threat of murder in places like Tanzania.